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Intravascular Papillary Endothelial Hyperplasia of the Maxillary Sinus in Patient with Tricuspid Atresia

  • Peter CookeEmail author
  • David Goldrich
  • Alfred Marc Iloreta
  • Abeer Salama
  • Raj Shrivastava
Case Report

Abstract

Intravascular papillary endothelial hyperplasia (IPEH) is a benign, highly vascularized, endothelial growth that can be mischaracterized as a malignancy. While hundreds of IPEH cases are reported, only four occurred in the maxillary sinus. We present the case of a 28-year-old male who underwent surgical resection of IPEH of the right maxillary sinus. An additional consideration was the patient’s condition of univentricular tricuspid atresia which contributed to chronic hypoxemia and polycythemia. After complete resection from the maxillary sinus, post-operational workup determined the lesion to be IPEH. Given the potential for misdiagnosis of IPEH, careful histopathologic evaluation is required in order to avoid improper treatment.

Keywords

Intravascular papillary endothelial hyperplasia Masson’s tumor Univentricular tricuspid atresia Hypercoagulable Sphenopalatine artery 

Notes

Compliance with Ethical Standards

Conflict of interest

The authors declare that they have no conflicts of interest or financial disclosures.

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Copyright information

© Springer Science+Business Media, LLC, part of Springer Nature 2019

Authors and Affiliations

  1. 1.Department of Otolaryngology- Head and Neck SurgeryIcahn School of Medicine at Mount SinaiNew YorkUSA
  2. 2.Department of PathologyIcahn School of Medicine at Mount SinaiNew YorkUSA
  3. 3.Department of NeurosurgeryIcahn School of Medicine at Mount SinaiNew YorkUSA

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