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Surgical Excision with Rotational Flap Reconstruction for Basosquamous Cell Carcinoma in Xeroderma Pigmentosa: A Case Report

  • Sharanabasappa Rudragouda Malipatil
  • Sriharsha Vijay JonnalagaddaEmail author
Clinical Report
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Abstract

Xeroderma pigmentosa (XP) is a rare autosomal recessive disorder which is characterized by a defect in nucleotide excision repair of DNA following exposure to UV radiation. This leads to hypersensitivity to sunlight causing pigmented skin lesions, photophobia and a 1000-fold increase in risk of developing cutaneous malignancies like basal cell carcinomas, squamous cell carcinomas and melanomas of head and neck. We present an interesting case of a 28 year old man with basosquamous cell carcinoma secondary to XP treated successfully with surgical excision and reconstruction with rotational flap technique.

Keywords

Rotational flap Basal cell carcinoma Xeroderma pigmentosa 

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Copyright information

© Association of Otolaryngologists of India 2018

Authors and Affiliations

  1. 1.Shri B.M Patil Medical College & Research CentreVijayapuraIndia

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