Dextrocardia and corrected transposition of the great arteries with rheumatic tricuspid stenosis: a unique association
- 9 Downloads
A 37-year-old lady presented with difficulty in breathing, which had progressively worsened in the last few months. Investigations revealed dextrocardia, congenitally corrected transposition of aorta, severe left atrioventricular valve stenosis with regurgitation, and right atrioventricular valve regurgitation. Left atrioventricular valve stenosis with thickening of leaflets and commissural fusion were suggestive of rheumatic valvular heart disease. She underwent left atrioventricular valve replacement and right atrioventricular valve repair with annuloplasty ring. This is a unique association of rheumatic valvular disease in corrected transposition of great arteries with dextrocardia. Morphology made surgical correction very challenging. Surgical correction of such case has not been reported in literature so far.
KeywordsDextrocardia Corrected transposition of great arteries Rheumatic valvular disease
Compliance with ethical standards
All procedures performed in studies involving human participants were in accordance with the ethical standards of the institutional and/or national research committee.
Informed consent was obtained from the patient for publication of this case report and accompanying images.
Conflict of interests
The authors declare that they have no competing interests.
- 1.Samanek M, Voriskova M. Congenital heart disease among 815,569 children born between 1980 and 1990 and their 15-year survival: a prospective Bohemia survival study. Pediatr Cardiol. 1999;20:411–17.Google Scholar
- 2.Graham TP Jr, Bernard YD, Mellen BG, et al. Long-term outcome in congenitally corrected transposition of the great arteries: a multi-institutional study. J Am Coll Cardiol. 2000;36:255–61.Google Scholar
- 3.Prieto LR, Hordof AJ, Secic M, Rosenbaum MS, Gersony WM. Progressive tricuspid valve disease in patients with congenitally corrected transposition of the great arteries. Circulation. 1998;98:997–1005.Google Scholar
- 4.Lundstrom U, Bull C, Wyse RK, Somerville J. The natural and “unnatural” history of congenitally corrected transposition. Am J Cardiol. 1990;65:1222–9Google Scholar
- 5.Waller BF, Howard J, Fess S. Pathology of tricuspid valve stenosis and pure tricuspid regurgitation—part II. Clin Cardiol. 1995;18:167–74.Google Scholar
- 6.Parale GP, Jeurkar VN. Situs inversus with dextrocardia with corrected transposition of great vessels with rheumatic systemic atrio-ventricular valve regurgitation: A 63-year-old adult survivor. Indian Heart J. 1994;46:353–44.Google Scholar
- 7.Kukreti BB, Ramakrishnan S, Bhargava B. Situs inversus with levocardia and congenitally corrected transposition of great vessels with rheumatic tricuspid valve stenosis and regurgitation. Heart Views. 2011;12:178-80.Google Scholar
- 8.Scherptong RW, Vliegen HW, Winter MM, et al. Tricuspid valve surgery in adults with a dysfunctional systemic right ventricle: repair or replace? Circulation. 2009;119:1467–72.Google Scholar