Anomalous left pulmonary artery: rare case, uncertain embryology and off-pump approach

  • Balram Babu RajanbabuEmail author
  • Raviraju Chigullapally
Case Report


Left pulmonary artery from descending aorta, left-sided arch and patent ductus arteriosus is a rare congenital anomaly. Only one such case has been reported before, which was repaired in the neonatal period and the authors suggested that current theories of embryology failed to explain such a combination. Early and often bilateral pulmonary vascular disease is common with such defects. We present an 8-month-old baby, with this anatomy, who was repaired using an off-pump approach, to minimize the risk of postoperative pulmonary hypertensive crisis and propose a “modified ontogenic theory” to explain the embryology.


Anomalous pulmonary artery Ontogenic theory Pulmonary artery hypertension 


Compliance with ethical standards

Conflict of interests

The authors declare that they have no conflict of interest.

Informed consent

Written consent was obtained from the patient’s parents.

Ethical concerns

Nil (case report).


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Copyright information

© Indian Association of Cardiovascular-Thoracic Surgeons 2018

Authors and Affiliations

  1. 1.Department of Pediatric Cardiac SurgeryApollo HospitalsHyderabadIndia

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