Deceiving spindle cell sarcoma of the heart

  • Anil AcharyaEmail author
  • Raamesh Koirala
  • Nivesh Rajbhandari
  • Nirmal Panthee
Case Report


Primary cardiac tumors are rare and when they occur, 75% are benign. Atrial myxomas having a good prognosis compromise 50% of all primary cardiac tumors. Only 25% of the primary cardiac tumors are malignant and 75% of these malignant tumors are sarcomas. Sarcomas often occur in young patients without any predisposing factors and tend to have very poor prognosis. We present an unfortunate case of a young female with high-grade spindle cell sarcoma. She was initially diagnosed to have mitral valve pathology and hypertrophic cardiomyopathy but confirmation of diagnosis was made only after a second operation and patient’s demise.


Cardiac neoplasm Mitral valve disease Sarcomas 


Compliance with ethical standards

Ethical statement

For this type of study, no formal consent is required; however, consent was taken from institutional review board for publishing this report in medical journals. This is a case report and this article does not contain any experimental study on human participants or animals performed by any of the authors.

Ethical approval

This article does not contain any studies with animals performed by any authors.

This is a case report and no experimental study was carried out on humans.

The identity of the patient has not been disclosed.

Informed consent was not taken from the patient as the decision to report the case was made only after the patient’s demise. However, permission was taken from the institutional review committee regarding publication of case in medical journals. This letter can be produced when required.

Conflict of interest

The authors declare that there is no conflict of interest.


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Copyright information

© Indian Association of Cardiovascular-Thoracic Surgeons 2018

Authors and Affiliations

  • Anil Acharya
    • 1
    Email author
  • Raamesh Koirala
    • 2
  • Nivesh Rajbhandari
    • 2
  • Nirmal Panthee
    • 2
  1. 1.Department of Cardiovascular and Thoracic SurgeryNepal MedicitiLalitpurNepal
  2. 2.Department of Cardiovascular SurgeryShahid Gangalal National Heart CentreKathmanduNepal

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