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Functionally univentricular heart with systemic venous anomalies: surgical palliation and pulmonary arterial reconstruction with a roll of left atrial appendage

  • Sachin Talwar
  • Robert Henry Anderson
  • Niwin George
  • Saurabh Kumar Gupta
  • Bharat Siddharth
  • Amolkumar Bhoje
  • Palleti Rajashekar
  • Shiv Kumar Choudhary
Case Report
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Abstract

In this report, we describe a 3-year-old patient with a functionally univentricular heart (UVH), who had a combination of double outlet right ventricle (DORV) along with an unrouteable interventricular communication (VSD), severe infundibular and pulmonary valvar stenosis, and severe left pulmonary artery (LPA) ostial stenosis. This patient also had an interrupted inferior caval vein (IVC) with bilateral superior caval veins (SVC). We were able to undertake a successful Kawashima procedure with interruption of the antegrade pulmonary blood flow, reconstructing the LPA using a pedicled roll of the left atrial appendage (LAA).

Keywords

Kawashima Pulmonary artery reconstruction Left atrial appendage 

Notes

Compliance with ethical standards

Conflict of interest

The authors declare that they have no conflict of interest.

Statement of human rights/ethical approval

All procedures performed in this study were in accordance with the ethical standards of the institutional and national research committee and with the 1964 Helsinki declaration and its later amendments or comparable ethical standards. For this study, formal consent was obtained.

Informed consent

Informed consent was obtained from all individual participants included in the study.

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Copyright information

© Indian Association of Cardiovascular-Thoracic Surgeons 2018

Authors and Affiliations

  1. 1.Cardiothoracic CentreAll India Institute of Medical SciencesNew DelhiIndia
  2. 2.Department of Cardiothoracic and Vascular SurgeryAll India Institute of Medical SciencesNew DelhiIndia
  3. 3.Institute of Genetic MedicineNewcastle UniversityNewcastle-upon-TyneUK
  4. 4.Birmingham Children’s HospitalBirminghamUK

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