Extranodal Marginal Zone B Cell (MALT) Lymphoma of the Esophagus
Approximately, one-quarter of all non-Hodgkin’s lymphoma cases manifest extranodally, half of which are located in the gastrointestinal tract. The majority of the cases are mature B cell neoplasms which arise in the stomach and are highly associated with H. pylori infection . In contrast, primary esophageal lymphoma is exceedingly rare, with only 18 cases reported to date in the world literature, nearly all of which are from Eastern Asia [2, 3]. Moreover, primary esophageal lymphoma does not have a clear association with H. pylori. Due to the rare occurrence of esophageal mucosa-associated lymphoid tissue (MALT) lymphoma, there is a paucity of data regarding clinical findings, endoscopic features, treatment regimen, and overall prognosis.
AK assisted with the manuscript preparation and editing. JHT drafted the manuscript and organized images. AMM provided histopathology data and images and edited the manuscript. KP edited the manuscript and provided the endoscopic and radiographic images and is the article guarantor.
Compliance with Ethical Standards
Conflict of Interest
The authors declare that they have no conflict of interest.
Informed consent was obtained for publication of the case details.
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