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Orbital Vasculitides–Differential Diagnosis

  • Gabriela M. EspinozaEmail author
  • Jessica L. Liu
Vasculitis (L Espinoza, Section Editor)
Part of the following topical collections:
  1. Topical Collection on Vasculitis

Abstract

Purpose of Review

The orbit is subject to a variety of vascular insults that manifest with both specific and nonspecific patterns of vision compromise. The aim of the following review is to highlight the ophthalmic clinical features of systemic vasculitides that most frequently involve the orbit and differentiate them from the most common non-vasculitic orbital disorders.

Recent Findings

New studies continue to explore the autoimmune nature of vasculitic disease and seek to determine optimal use of newer therapies such as biologic agents.

Summary

The pattern of ocular involvement in the context of clinical history allows the knowledgeable physician to distill a differential diagnosis into a specific or likely cause. Establishing a diagnosis in a timely fashion allows for a custom-tailored approach to therapy.

Keywords

Vasculitis Behcet’s disease IgG4 disease Cogan’s disease Granulomatosis with polyangiitis Takayasu arteritis 

Notes

Acknowledgments

The authors would like to thank Dr. Gabriel Andrade from the Federal University of Sao Paulo–UNIFESP for his photographic contribution to this paper. We also thank Dr. Eduardo B. Rodrigues for his assistance.

Compliance with Ethical Standards

Conflict of Interest

The authors declare that they have no conflict of interest.

Human and Animal Rights and Informed Consent

This article does not contain any studies with human or animal subjects performed by any of the authors.

References

Papers of particular interest, published recently, have been highlighted as: • Of importance •• Of major importance

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© Springer Science+Business Media, LLC, part of Springer Nature 2019

Authors and Affiliations

  1. 1.Department of OphthalmologySaint Louis University School of MedicineSaint LouisUSA

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