Pacing in Patients with Congenital Heart Disease: When Is It Helpful and When Is It Harmful?

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Purpose of Review

Pacing in pediatric and adult patients with congenital heart disease requires careful evaluation and thoughtful planning. Review of current guidelines with assessment of risk/benefit must be performed along with planning on a case-by-case basis in order to achieve maximal success and reduce risk in this specialized population of patients that is rapidly increasing in size.

Recent Findings

Guidelines for pacing in pediatric and congenital heart disease patients span many years. Most recent consensus and summary guidelines address pacing in adult patients with or without congenital heart disease. Pediatric recommendations from prior documents must be included in current decision-making.


Pacing in pediatric and congenital heart disease patients is important therapy. Creation of an individualized plan of care with attention to risk/benefit decision-making regarding when and how to pace is critical in this population to maximize beneficial outcome.

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Fig. 1


    Papers of particular interest, published recently, have been highlighted as: • Of importance •• Of major importance

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    Correspondence to Salim F. Idriss.

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    M. David Weiland and Salim F. Idriss declare that they have no conflict of interest.

    Zebulon Spector reports personal fees from Janssen Research & Development.

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    This article is part of the Topical Collection on Congenital Heart Disease.

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    Weiland, M.D., Spector, Z. & Idriss, S.F. Pacing in Patients with Congenital Heart Disease: When Is It Helpful and When Is It Harmful?. Curr Cardiol Rep 22, 5 (2020) doi:10.1007/s11886-020-1253-2

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    • Congenital heart disease
    • Pediatric
    • ACHD
    • Pacing
    • Complete heart block
    • Bradycardia