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Surgical management of large undifferentiated cardiac sarcoma involving the right ventricle to pulmonary trunk

  • Hiroshi FurukawaEmail author
  • Takeshi Honda
  • Takahiko Yamasawa
  • Yuji Kanaoka
  • Kazuo Tanemoto
Case Report
  • 39 Downloads

Abstract

A large intra-cardiac tumor from the right ventricle to pulmonary trunk was detected by contrast-enhanced computed tomography and transthoracic echocardiography in a 59-year-old woman with progressive dyspnea on effort and acute congestive right-sided heart failure. Emergent surgical management was performed with cardiopulmonary bypass under cardiac arrest, however, tumor resection was incomplete, because it originated from the interventricular septum. Concomitant tricuspid valve replacement using a bioprosthesis was required due to the involvement of the septal leaflet of the tricuspid valve. Although large pulmonary thromboembolism was initially suspected, a pathological examination confirmed undifferentiated cardiac sarcoma. The patient did not consent to additional neoadjuvant chemotherapy or radiation therapy. After palliative surgical management, she was discharged. Recurrence rapidly progressed and the patient died approximately 2 months after surgery. We herein present a successful palliative surgical case of large cardiac undifferentiated sarcoma originating from the intraventricular septum and involving the right ventricle to pulmonary trunk.

Keywords

Cardiac sarcoma Undifferentiated sarcoma Congestive heart failure Tricuspid valve replacement Right ventricle 

Notes

Compliance with ethical standards

Conflict of interest

All authors declare that they have no conflict of interest.

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Copyright information

© The Japanese Association for Thoracic Surgery 2019

Authors and Affiliations

  • Hiroshi Furukawa
    • 1
    Email author
  • Takeshi Honda
    • 1
  • Takahiko Yamasawa
    • 1
  • Yuji Kanaoka
    • 1
  • Kazuo Tanemoto
    • 1
  1. 1.Department of Cardiovascular SurgeryKawasaki Medical SchoolKurashikiJapan

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