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Variant scimitar syndrome with intralobar pulmonary sequestration containing adenocarcinoma

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Abstract

Scimitar syndrome is a rare congenital anomaly in which the right lung is hypoplastic and a scimitar vein is draining into the inferior vena cava. It is known to be sometimes complicated with pulmonary sequestration. However, a right single pulmonary vein draining normally into the left atrium is rare. Here, we report a case of variant scimitar syndrome complicated by intralobar pulmonary sequestration containing an adenocarcinoma. In this case, the aberrant arteries from the abdominal aorta were ligated and the pulmonary sequestration containing adenocarcinoma was completely removed through wedge resection. Twenty months after the surgery, the patient was alive without cancer recurrence. An elaborate preoperative plan is important for safety in cases with vascular malformation.

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Correspondence to Hiroshi Date.

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Video 1. The wedge resection of intralobar pulmonary sequestration through VATS was performed. The aberrant artery arising from the abdominal aorta was divided into two vessels in the right thoracic cavity, and each artery was ligated first. Then, the boundary between normal lung parenchyma and intralobar pulmonary sequestration was divided with linear stapler. Finally, the resected specimen was introduced in a bag and removed from the thorax cavity. (MPG 283336 KB)

Video 1. The wedge resection of intralobar pulmonary sequestration through VATS was performed. The aberrant artery arising from the abdominal aorta was divided into two vessels in the right thoracic cavity, and each artery was ligated first. Then, the boundary between normal lung parenchyma and intralobar pulmonary sequestration was divided with linear stapler. Finally, the resected specimen was introduced in a bag and removed from the thorax cavity. (MPG 283336 KB)

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Kayawake, H., Motoyama, H. & Date, H. Variant scimitar syndrome with intralobar pulmonary sequestration containing adenocarcinoma. Gen Thorac Cardiovasc Surg 68, 74–76 (2020) doi:10.1007/s11748-019-01098-3

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Keywords

  • Pulmonary sequestration
  • Scimitar syndrome
  • Variant
  • Adenocarcinoma