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General Thoracic and Cardiovascular Surgery

, Volume 67, Issue 12, pp 1089–1092 | Cite as

A rare resected case of pulmonary rhabdomyosarcoma

  • Yuki Nishioka
  • Shinya Tane
  • Wataru Nishio
  • Hiroki Tanaka
  • Hiroyuki Ogawa
  • Yoshitaka Kitamura
  • Toshiko Sakuma
  • Masahiro Yoshimura
Case Report
  • 113 Downloads

Abstract

Rhabdomyosarcoma is a well-known neoplasm in children that frequently occurs in the extremities, the head and neck region, and the genitourinary tract. To the best of our knowledge, pulmonary primary rhabdomyosarcoma in adults is exceedingly rare, and few resected cases have been reported. We report a case of pulmonary primary rhabdomyosarcoma that was surgically resected then treated with adjuvant chemotherapy (vincristine, actinomycin-D and cyclophosphamide). At 9 months after surgery, the patient is free from disease. Although the prognosis of rhabdomyosarcoma is unfavorable, surgical resection and adjuvant therapy could be a potential treatment strategy for pulmonary primary rhabdomyosarcoma.

Keywords

Rhabdomyosarcoma Surgery Lung 

Notes

Compliance with ethical standards

Conflict of interest

The authors have declared that no conflict of interest exists.

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Copyright information

© The Japanese Association for Thoracic Surgery 2019

Authors and Affiliations

  • Yuki Nishioka
    • 1
  • Shinya Tane
    • 1
  • Wataru Nishio
    • 1
  • Hiroki Tanaka
    • 1
  • Hiroyuki Ogawa
    • 1
  • Yoshitaka Kitamura
    • 1
  • Toshiko Sakuma
    • 2
  • Masahiro Yoshimura
    • 1
  1. 1.Division of Chest SurgeryHyogo Cancer CenterAkashiJapan
  2. 2.Division of PathologyHyogo Cancer CenterAkashiJapan

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