Case report: hypertrophic pachymeningitis associated with Sjögren’s syndrome
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Sjögren syndrome (SS) is a systemic chronic autoimmune disorder characterized by lymphocytic infiltrates into the exocrine organs, particularly the parotid and lacrimal glands that results in typically distinct symptoms which manifest as xerophthalmia (dry eyes) and xerostomia (dry mouth). In addition, various organs could be involved with numerous extraglandular features, such as arthritis, Raynaud phenomenon, lymphoma, pulmonary disease, gastrointestinal disease, and neurological disease. Among the neurological diseases, sensory polyneuropathy is known to be the most common pattern, and mononeuropathy multiplex, polyradiculopathy, symptomatic dysautonomia, cranial neuropathy, myopathy, and central nervous system (CNS) involvement are less common .
The prevalence of CNS involvement in SS in a recent study was 67.5% . However, a substantial variability in the reported prevalence exists because of the selection and referral bias . Although the wide spectrum of CNS...
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The authors declare that they have no conflict of interest.
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