A case of primary angiitis of the central nervous system presenting with diffuse cerebral microbleeds and recurrent intracranial hemorrhage
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Primary angiitis of the central nervous system (PACNS) refers to a rare single-organ vasculitis that results in inflammation and destruction of the small and medium vessels restricted to brain, spinal cord, and the meninges . It is one of the foremost diagnostic challenges since it produces vague and unspecific signs and symptoms, presents variable laboratory and imaging manifestations, and requires extensive investigation to rule out various differential diagnoses. Biopsy of the brain remains the gold standard diagnostic test. Here, we present a case of PACNS presenting with cerebral microbleeds (CMBs) and recurrent intracranial hemorrhage (ICH).
This research was supported by grants from the Shandong provincial key research and development plan (2018GSF121009).
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Conflict of interest
The authors declare that they have no conflict of interest.
Informed consent was obtained from the patient.
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