Neurological Sciences

, Volume 39, Issue 9, pp 1603–1605 | Cite as

Dyke-Davidoff-Masson syndrome: an unusual case of late diagnosis

  • Ana Carolina B. Duarte
  • Bruno Camporeze
  • Renata P. BuainainEmail author
Letter to the Editor

Dear Editor-in-Chief,

Dyke-Davidoff-Masson syndrome (DDMS) is a rare neurological disorder usually observed during childhood and classically characterized by epilepsy, hemiparesia/hemiplegia, facial asymmetry, and mental retardation. It is radiologically characterized by partial or diffuse cerebral hemiatrophy [1, 2].

DDMS can be classified as congenital when it occurs before 2 years of age, typically resulting from intrauterine or neonatal vascular insults, whereas the acquired form can arise due to a variety of brain insults, including asphyxia, traumas, infections, prolonged febrile seizures, ischemia, and brain hemorrhages. The onset and presentation are variable [2]. It is our intention to expose an unusual case in which diffuse cerebral hemiatrophy occurred mid-life, accompanying a previous history of mild neurological symptoms. We explore the clinical features and radiological findings and propose an unusual evolution and late diagnosis of acquired DDMS.

A 48-year-old male was...


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Copyright information

© Springer-Verlag Italia S.r.l., part of Springer Nature 2018

Authors and Affiliations

  • Ana Carolina B. Duarte
    • 1
  • Bruno Camporeze
    • 1
  • Renata P. Buainain
    • 2
    Email author
  1. 1.Medical Student, Sao Francisco University – Medical SchoolSão PauloBrasil
  2. 2.Professor of Neurology, Neurology DepartmentSão Francisco University – Medical SchoolSão PauloBrasil

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