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Recurrent meningitis and cerebrospinal fluid leak–two sides of the same vestibulocochlear defect: report of three cases

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Cochlear dysplasia is a rare congenital anomaly. However, early detection of this anomaly can prevent serious consequences. We describe three cases of cochlear dysplasia that presented with recurrent meningitis and cerebro-spinal fluid (CSF) leak in children in which early diagnosis prevented further complications.

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Correspondence to M. Ben-Shoshan.

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Ben-Shoshan, M., DeRowe, A., Grisaru-Soen, G. et al. Recurrent meningitis and cerebrospinal fluid leak–two sides of the same vestibulocochlear defect: report of three cases. Eur J Pediatr 166, 269–272 (2007). https://doi.org/10.1007/s00431-006-0236-7

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  • Cochlear dysplasia
  • Mondini malformation
  • Meningitis
  • CSF leak