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A case of severe Pierre Robin sequence with failure to thrive and tachycardia resolved after redo-fundoplication and hiatoplasty

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Abstract

We report an infant suffering from Pierre Robin sequence complicated by gastro-oesophageal reflux and failure to thrive, which were resistant to conservative therapy and a hemifundoplication. Gastro-oesophageal reflux was accompanied by supraventricular tachycardia, treated with propafenone. Tachycardia may be present in Pierre Robin sequence as a consequence of cardiac parasympathetic imbalance. The patient recovered completely from the gastro-oesophageal reflux and tachycardia after redo-fundoplication (Nissen) and a hiatoplasty were performed. Conclusion:This case shows that a thorough search for gastro-oesophageal reflux is indicated in each case of Pierre Robin sequence with failure to thrive.

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Abbreviations

FTT :

failure to thrive

GER :

gastro-oesophageal reflux

GERD :

gastro-oesophageal reflux disease

PRS :

Pierre Robin sequence

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Correspondence to Klaus-Peter Zimmer.

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Reinshagen, K., Schellscheidt, J. & Zimmer, K. A case of severe Pierre Robin sequence with failure to thrive and tachycardia resolved after redo-fundoplication and hiatoplasty. Eur J Pediatr 164, 573–576 (2005). https://doi.org/10.1007/s00431-005-1682-3

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Keywords

  • Gastro-oesophageal reflux
  • Pierre Robin sequence
  • Tachycardia