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Pendular nystagmus in progressive ataxia and palatal tremor

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Acknowledgments

The authors thank Dr. Erik Ulmer for his technical advice and the patient for his willing collaboration and sympathy.

Conflict of interest

None reported.

Author information

Correspondence to R. Bassani.

Electronic supplementary material

Below is the link to the electronic supplementary material.

Video 1 The video demonstrates the presence of marked disequilibrium both in the static tests as the Single Leg Stance and in the dynamic tests as in Tandem Walking. (MPG 13090 kb)

Video 2 The video presents the principal cerebellar coordination tests to the superior and inferior limbs. The coordination tests are basically unimpaired in this patient. (MPG 4130 kb)

Video 3 The ocular oscillations are barely recognizable at clinical examination (part 1), while the nystagmus is clearly demonstrated through the infrared video-oculography. The nystagmus develops preferentially in the vertical plane. A secondary rotational counter-clockwise component can be identified (part 2). The palatal tremor is symmetrical, although it is occasionally lateralized to the left side (part 3). (MPG 3510 kb)

Video 1 The video demonstrates the presence of marked disequilibrium both in the static tests as the Single Leg Stance and in the dynamic tests as in Tandem Walking. (MPG 13090 kb)

Video 2 The video presents the principal cerebellar coordination tests to the superior and inferior limbs. The coordination tests are basically unimpaired in this patient. (MPG 4130 kb)

Video 3 The ocular oscillations are barely recognizable at clinical examination (part 1), while the nystagmus is clearly demonstrated through the infrared video-oculography. The nystagmus develops preferentially in the vertical plane. A secondary rotational counter-clockwise component can be identified (part 2). The palatal tremor is symmetrical, although it is occasionally lateralized to the left side (part 3). (MPG 3510 kb)

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Bassani, R., Mariotti, C., Nanetti, L. et al. Pendular nystagmus in progressive ataxia and palatal tremor. J Neurol 258, 1877–1879 (2011). https://doi.org/10.1007/s00415-011-6007-z

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Keywords

  • Spinocerebellar Ataxia
  • Inferior Olive
  • Superior Cerebellar Peduncle
  • Friedreich Ataxia
  • Progressive Ataxia