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The authors thank Dr. Erik Ulmer for his technical advice and the patient for his willing collaboration and sympathy.
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Video 3 The ocular oscillations are barely recognizable at clinical examination (part 1), while the nystagmus is clearly demonstrated through the infrared video-oculography. The nystagmus develops preferentially in the vertical plane. A secondary rotational counter-clockwise component can be identified (part 2). The palatal tremor is symmetrical, although it is occasionally lateralized to the left side (part 3). (MPG 3510 kb)
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Bassani, R., Mariotti, C., Nanetti, L. et al. Pendular nystagmus in progressive ataxia and palatal tremor. J Neurol 258, 1877–1879 (2011). https://doi.org/10.1007/s00415-011-6007-z
- Spinocerebellar Ataxia
- Inferior Olive
- Superior Cerebellar Peduncle
- Friedreich Ataxia
- Progressive Ataxia