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Vaskulitis-Mimics

  • I. KötterEmail author
  • E. Reinhold-Keller
Leitthema
  • 41 Downloads

Zusammenfassung

Vaskulitis-Mimics sind von den primären und sekundären Vaskulitiden gemäß der Chapel-Hill-Nomenklatur abzugrenzen. Ihre Klinik ähnelt der einer Vaskulitis kleiner oder mittlerer, manchmal auch großer Gefäße und imitiert so die entsprechenden klassischen Krankheitsbilder. Ursache sind teilweise genetische Mutationen, Embolisationssyndrome, Infektionen oder auch Substanzabusus. Auch B‑Zell-Lymphome können eine Vaskulitis imitieren. In der vorliegenden Arbeit werden die entsprechenden Vaskulitis-Mimics zusammengefasst.

Schlüsselwörter

Chapel-Hill-Nomenklatur B-Zell-Lymphome Granulomatose mit Polyangiitis Behçet-Syndrom Fehlendes Therapieansprechen 

Vasculitis mimics

Abstract

Vasculitis mimics need to be differentiated from primary and secondary vasculitides as described in the Chapel Hill nomenclature. The clinical symptomatology resembles that of vasculitis of small and medium, rarely also large vessels and hence imitates the classical vasculitic disorders. Pathogenetically, the causes are partly genetic mutations, embolization syndromes, infections and substance abuse. Also, B‑cell lymphomas can mimic vasculitis. The present manuscript summarizes the vasculitis mimics.

Keywords

Chapel Hill nomenclature B-cell lymphoma Granulomatosis with polyangiitis Behcet syndrome Lack of response to treatment 

Notes

Einhaltung ethischer Richtlinien

Interessenkonflikt

I. Kötter und E. Reinhold-Keller geben an, dass kein Interessenkonflikt besteht.

Dieser Beitrag beinhaltet keine von den Autoren durchgeführten Studien an Menschen oder Tieren. Für Bildmaterial oder anderweitige Angaben innerhalb des Manuskripts, über die Patienten zu identifizieren sind, liegt von ihnen und/oder ihren gesetzlichen Vertretern eine schriftliche Einwilligung vor.

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Copyright information

© Springer Medizin Verlag GmbH, ein Teil von Springer Nature 2019

Authors and Affiliations

  1. 1.Rheumatologie, Klinische Immunologie, NephrologieAsklepios Klinik AltonaHamburgDeutschland
  2. 2.Internistisch-rheumatologische PraxisHamburgDeutschland

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