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Pediatric Surgery International

, Volume 35, Issue 2, pp 239–242 | Cite as

Sacral agenesis and fecal incontinence: how to increase the index of suspicion

  • Lindel Dewberry
  • Alberto Peña
  • David Mirsky
  • Jill Ketzer
  • Andrea BischoffEmail author
Original Article

Abstract

Purpose

Sacral abnormalities range from missing the coccyx, a few sacral vertebrae, or hemi-sacrum, to complete absence with fused iliac bones. The purpose of this study was to review the association between sacral agenesis and fecal incontinence to help inform patient prognosis.

Methods

A retrospective review was performed of patients who presented for bowel management due to sacral agenesis at a tertiary care children’s hospital between 2016 and 2017 (n = 10). Data collection included: gender, time of diagnosis, sacral ratio, and associated anomalies. Patients with anorectal malformation and sacrococcygeal teratomas were excluded.

Results

Four patients were female. Seven patients had a delayed diagnosis ranging from 22 months of age to 9 years. Most common symptoms included failure of age-appropriate toilet training and severe diaper rash. The sacral ratio was zero (6), 0.3 and 0.4 (2), and hemi-sacrum (2). Associated anomalies were present in five patients.

Conclusion

Sacral abnormalities should be suspected in patients who present with early severe diaper rash and those who fail to toilet train. An abdominal radiograph can evaluate the sacrum, when the sacral ratio is 0.4 or less, parents should be counseled regarding fecal incontinence and neurogenic bladder.

Keywords

Sacral agenesis Fecal incontinence Sacral abnormalities Caudal regression 

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Copyright information

© Springer-Verlag GmbH Germany, part of Springer Nature 2018

Authors and Affiliations

  • Lindel Dewberry
    • 1
  • Alberto Peña
    • 2
  • David Mirsky
    • 3
  • Jill Ketzer
    • 2
  • Andrea Bischoff
    • 2
    Email author
  1. 1.Department of SurgeryUniversity of ColoradoAuroraUSA
  2. 2.Department of Pediatric Surgery, International Center for Colorectal and Urogenital CareChildren’s Hospital Colorado, Anschutz Medical CampusAuroraUSA
  3. 3.Department of RadiologyChildren’s Hospital ColoradoAuroraUSA

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