Child's Nervous System

, Volume 35, Issue 9, pp 1443–1444 | Cite as

Shifting epidemiology of single-suture craniosynostosis and the need for a more granular ICD classification system: a national survey of members from the American Society of Pediatric Neurosurgeons (ASPN) and the American Society of Craniofacial Surgeons (ASCFS)

  • Santiago R. Gonzalez
  • Alex Han
  • Michael S. GolinkoEmail author
Letter to the Editor

Dear Editor:

The purpose of our letter is to bring attention to the national epidemiological studies who reported an increase in the incidence of metopic craniosynostosis and to raise awareness about the importance of developing improved International Classification of Disease (ICD) codes for craniosynostosis [1, 2, 3]. Reports of epidemiological shifts in single-suture synostosis are not limited to the USA. In the last decade, epidemiological studies across Europe have also reported a similar increase in the incidence of metopic craniosynostosis. A study done in France by DiRocco et al. revealed almost a 4-fold increase in metopic craniosynostosis, compared with a 1.7-fold increase in sagittal craniosynostosis [4]. A nine-year study using data from centers throughout Europe found a statistically significant increase in the incidence of metopic cases in both absolute numbers and in comparison with other craniosynostosis subtypes [5]. As a means to provide an insight into the views of...


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Conflict of interest

The authors declare that they have no conflict of interest.


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Copyright information

© Springer-Verlag GmbH Germany, part of Springer Nature 2019

Authors and Affiliations

  1. 1.University of Arkansas for Medical SciencesLittle RockUSA
  2. 2.Houston Methodist HospitalHoustonUSA
  3. 3.Department of Plastic SurgeryVanderbilt University Medical CenterNashvilleUSA
  4. 4.Monroe Carell Jr. Children’s Hospital at VanderbiltNashvilleUSA

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