Child's Nervous System

, Volume 35, Issue 2, pp 355–362 | Cite as

A rare clinical presentation: a pleomorphic xanthoastrocytoma presenting with intracerebral haemorrhage and metastasizing vigorously—case report and review of the literature

  • Gülden Demirci OtluoğluEmail author
  • M. Memet Özek
Case Report


Metastasis of an intracranial tumour is not a common situation in our daily neurosurgical practice. Pleomorphic xanthoastrocytoma is also a rare glial tumour with relatively a favourable prognosis among other CNS pathologies. Here, we present an anaplastic pleomorphic xanthoastrocytoma case which shows both haematogenous and lymphatic metastasis which is described first time in the up-to-date literature. Our case is a 17-year-old male operated for a right occipital intra-axial lesion with a diagnosis of anaplastic pleomorphic xanthoastrocytoma which recurs 5 years later and metastasize vigorously through haematogenous and lymphatic routes. A rare-presenting symptom for this pathology is also intracerebral haemorrhage. This is the ninth case report in the literature which presents initially with this entity.


Pleomorphic xanthoastrocytoma Haemorrhage Anaplastic PXA Lesion 



The authors thank Mrs. Özlem Yapıcıer, MD for her contribution for editing figures and details related to pathological headings.

Compliance with ethical standards

Conflict of interest

The authors declare that they have no conflict of interest.


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Copyright information

© Springer-Verlag GmbH Germany, part of Springer Nature 2018

Authors and Affiliations

  1. 1.Division of Pediatric NeurosurgeryAcıbadem University School of MedicineÜsküdar/İstanbulTurkey

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