Skeletal Radiology

, Volume 26, Issue 3, pp 191–194 | Cite as

Maffucci’s syndrome associated with spindle cell hemangioendothelioma

  • Masanori Hisaoka
  • Takatoshi Aoki
  • Hiromi Kouho
  • Hirofumi Chosa
  • Hiroshi Hashimoto
Case Reports


The case of a 49-year-old man with Maffucci’s syndrome, who developed multiple spindle cell hemangioendotheliomas, is presented. The case provides support for recent reports suggesting an association between this peculiar vascular lesion and skeletal enchondromatosis.

Key words

Maffucci’s syndrome Spindle cell hemangioendothelioma Enchondromatosis Hemangioma Histopathology 


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Copyright information

© International Skeletal Society 1997

Authors and Affiliations

  • Masanori Hisaoka
    • 1
  • Takatoshi Aoki
    • 1
  • Hiromi Kouho
    • 1
  • Hirofumi Chosa
    • 2
  • Hiroshi Hashimoto
    • 1
  1. 1.Department of Pathology and Oncology, School of MedicineUniversity of Occupational and Environmental HealthKitakyushuJapan
  2. 2.Department of OrthopedicsKyushu Rosai HospitalKitakyushuJapan

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