Skeletal Radiology

, Volume 26, Issue 3, pp 184–187 | Cite as

Primitive neuroectodermal tumor in a child with tuberous sclerosis

  • Bernard W. Hindman
  • Harmandeep K. Gill
  • Craig W. Zuppan
Case Reports


The case of a 13-year-old boy with tuberous sclerosis and primitive neuroectodermal tumor of bone is presented. A pathogenetic association between these two entities is postulated, the unifying underlying mechanism being a maldevelopment of the neural crest, or neurocristopathy.

Key words

Primitive neuroectodermal tumor Tuberous sclerosis Neurocristopathy 


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Copyright information

© International Skeletal Society 1997

Authors and Affiliations

  • Bernard W. Hindman
    • 1
  • Harmandeep K. Gill
    • 1
  • Craig W. Zuppan
    • 2
  1. 1.Department of RadiologyLoma Linda University School of MedicineLoma LindaUSA
  2. 2.Department of PathologyLoma Linda University School of MedicineLoma LindaUSA

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