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Skeletal Radiology

, Volume 47, Issue 11, pp 1567–1570 | Cite as

The lucent (CT) and enhancing (MR) rim, a sign of Paget’s disease of the skull: case report

  • Myriame Bou Antoun
  • Salim Kemel
  • Marc Polivka
  • Damien Bresson
  • Jean-Denis Laredo
Case Report

Abstract

Osteoporosis circumscripta is sometimes observed at the skull vault and corresponds to the initial stage of Paget’s disease of the bone. Differentiating osteoporosis circumscripta from other reasons for osteolytic images of the vault may be difficult. We report a case of osteoporosis circumscripta of the frontal bone. A lucent rim seen on CT scan, which was enhanced on gadolinium-enhanced MRI, delineated the abnormal bone. The patient was a 50-year-old woman who had CT scans of the skull for chronic sinusitis. Pathology examination showed typical bone changes of Paget’s disease. The lucent and enhancing rim sign may help in differentiating Paget’s disease from other conditions.

Keywords

Paget’s disease of bone Skull CT MRI 

Notes

Compliance with ethical standards

Conflict of interest

The authors declare that they have no conflicts of interest.

Disclosure

Nothing to declare.

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Copyright information

© ISS 2018

Authors and Affiliations

  • Myriame Bou Antoun
    • 1
  • Salim Kemel
    • 1
  • Marc Polivka
    • 2
  • Damien Bresson
    • 3
  • Jean-Denis Laredo
    • 1
  1. 1.Department of RadiologyHôpital Lariboisière, Assistance Publique-Hôpitaux de Paris (AP-HP) and Université Paris-DiderotParisFrance
  2. 2.Department of PathologyHôpital Lariboisière, Assistance Publique-Hôpitaux de Paris (AP-HP) and Université Paris-DiderotParisFrance
  3. 3.Department of NeurosurgeryHôpital Lariboisière, Assistance Publique-Hôpitaux de Paris (AP-HP) and Université Paris-DiderotParisFrance

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