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Pediatric Radiology

, Volume 48, Issue 9, pp 1307–1323 | Cite as

Thoracoabdominal imaging of tuberous sclerosis

  • Cara E. Morin
  • Nicholas P. Morin
  • David N. Franz
  • Darcy A. Krueger
  • Andrew T. Trout
  • Alexander J. Towbin
Pediatric Body MRI
  • 161 Downloads

Abstract

Imaging of tuberous sclerosis complex has rapidly evolved over the last decade in association with increased understanding of the disease process and new treatment modalities. Tuberous sclerosis complex is best known for the neurological symptoms and the associated neuroimaging findings, and children with tuberous sclerosis complex require active surveillance of associated abnormalities in the chest, abdomen and pelvis. Common findings that require regular imaging surveillance are angiomyolipomas in the kidneys and lymphangioleiomyomatosis in the chest. However multiple rarer associations have been attributed to tuberous sclerosis complex and should be considered by radiologists reviewing any imaging in these children. In this review the authors discuss the spectrum of imaging findings in people with tuberous sclerosis complex, focusing on MR imaging findings in the chest, abdomen and pelvis.

Keywords

Angiomyolipoma Children Magnetic resonance imaging Tuberous sclerosis complex 

Notes

Compliance with ethical standards

Conflicts of interest

Drs Franz and Krueger declared potential conflicts of interest.

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Copyright information

© Springer-Verlag GmbH Germany, part of Springer Nature 2018

Authors and Affiliations

  • Cara E. Morin
    • 1
  • Nicholas P. Morin
    • 2
  • David N. Franz
    • 3
  • Darcy A. Krueger
    • 3
  • Andrew T. Trout
    • 1
  • Alexander J. Towbin
    • 1
  1. 1.Department of RadiologyCincinnati Children’s Hospital Medical CenterCincinnatiUSA
  2. 2.Division of Emergency MedicineCincinnati Children’s Hospital Medical CenterCincinnatiUSA
  3. 3.Division of NeurologyCincinnati Children’s Hospital Medical CenterCincinnatiUSA

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