Pediatric Cardiology

, Volume 40, Issue 8, pp 1748–1751 | Cite as

Two Cases of a Prenatally Diagnosed Double Aortic Arch with Postnatal Obliteration of the Distal Left Aortic Arch

  • Tam T. DoanEmail author
  • Alicia Wang
  • Brooke Davey
  • Shailendra Upadhyay
  • Olga Toro-Salazar
Case Report


We report two cases of prenatally diagnosed double aortic arch with dominant right arch and a left-sided ductus arteriosus, consistent with a complete vascular ring. Postnatal transthoracic echocardiogram and cardiac magnetic resonance imaging demonstrated a spontaneous closure of the ductus arteriosus and obliteration of the left aortic arch distal to the origin of the left subclavian artery in both cases. Spontaneous closure of the ductus arteriosus involving extended ductal tissue in the left aortic arch likely led to obliteration of the distal left arch after birth. One patient presented with recurrent symptoms suggestive of dysphagia and underwent a successful surgical repair of the vascular ring with resolution of symptoms. The other patient has been asymptomatic and is 4 years old at the time of this report.


Vascular ring Double aortic arch Atretic left aortic arch Fetal echocardiography Cardiac magnetic resonance imaging 


Compliance with Ethical Standards

Conflict of interest

This study has no financial aid. Authors declare that there is no conflict of interest.

Ethical Approval

All procedures performed in studies involving human participants were in accordance with the ethical standards of the institutional and/or national research committee and with the 1964 Helsinki declaration and its later amendments or comparable ethical standards.

Informed Consent

Informed consent was not obtained for this case report.

Supplementary material

Supplementary file1 (MP4 3890 kb)

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Supplementary file2 (AVI 23958 kb)


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Copyright information

© Springer Science+Business Media, LLC, part of Springer Nature 2019

Authors and Affiliations

  1. 1.The Lillie Frank Abercrombie Section of Cardiology, Department of Pediatrics, Texas Children’s HospitalBaylor College of MedicineHoustonUSA
  2. 2.Department of Pediatric CardiologyConnecticut Children’s Medical Center and University of Connecticut School of MedicineHartfordUSA

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