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Pediatric Cardiology

, Volume 34, Issue 8, pp 2086–2088 | Cite as

Double-Outlet Right Ventricle With an Intact Ventricular Septum: A Unique Stage 1 Palliation

  • Kiran K. MallulaEmail author
  • Neil D. Patel
  • Ziyad M. Hijazi
  • Swosti Joshi
  • Zahra Naheed
Case Report
  • 182 Downloads

Abstract

This report describes a case of double-outlet right ventricle with intact ventricular septum diagnosed in a newborn male. The initial diagnosis was made by echocardiography. The baby underwent a hybrid procedure including pulmonary artery banding and stenting of the patent ductus arteriosus. He subsequently underwent stenting of the atrial communication. The patient was discharged at 55 days of life with the intent to perform palliative repair at a later date.

Keywords

Double-outlet right ventricle Hybrid Intact ventricular septum Stage 1 procedure 

Supplementary material

Movie clip 1

Subcostal long-axis sweep demonstrating a dilated left atrium with a hypertrophied left ventricle. The interatrial septum is tenting to the right with a restrictive foramen ovale (44.1 mb)

Movie clip 2

Subcostal short-axis sweep demonstrating a dilated left atrium with a crowded right ventricle, with both the aorta and pulmonary artery arising from the right ventricle (32.1 mb)

246_2013_741_MOESM3_ESM.avi (2.8 mb)
Movie clip 3 Suprasternal view demonstrating the reversal of flow in the arch of the aorta, which also is hypoplastic (2.75 mb)

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Copyright information

© Springer Science+Business Media New York 2013

Authors and Affiliations

  • Kiran K. Mallula
    • 1
    Email author
  • Neil D. Patel
    • 1
  • Ziyad M. Hijazi
    • 1
  • Swosti Joshi
    • 2
  • Zahra Naheed
    • 2
  1. 1.Rush Center for Congenital and Structural Heart DiseaseRush University Medical CenterChicagoUSA
  2. 2.John H. Stoger, Jr. Hospital of Cook CountyChicagoUSA

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