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Isolated Cleft Mitral Valve With Severe Regurgitation Resulting in a Left Inferior Pulmonary Vein Varix Diagnosed From Cardiovascular Magnetic Resonance Imaging

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Abstract

Isolated cleft mitral valve (ICMV) is a rare entity not known to be related to pulmonary atresia with ventricular septal defect (PA-VSD). This report describes the use of cardiovascular magnetic resonance (CMR) imaging to diagnose ICMV in a patient with repaired PA-VSD who presented with incidental severe mitral regurgitation (MR) on follow-up echocardiography. An associated pulmonary varix secondary to the severe MR also was shown by CMR.

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Author information

Correspondence to Lynette L. S. Teo.

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Move clip 2 Four-chamber cine gradient echo images showing an eccentric mitral regurgitant jet directed posteriorly toward the confluence between the left inferior pulmonary vein (LIPV) and left atrium (LA). The left cardiac chambers are dilated. (AVI 370 kb)

Movie clip 1 Short-axis cine gradient echo images showing the deep cleft at the anterior mitral valve leaflet directed toward the left ventricular outflow tract. (AVI 426 kb)

Move clip 2 Four-chamber cine gradient echo images showing an eccentric mitral regurgitant jet directed posteriorly toward the confluence between the left inferior pulmonary vein (LIPV) and left atrium (LA). The left cardiac chambers are dilated. (AVI 370 kb)

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Teo, L.L.S., Hia, C.P.P., Ling, L.H. et al. Isolated Cleft Mitral Valve With Severe Regurgitation Resulting in a Left Inferior Pulmonary Vein Varix Diagnosed From Cardiovascular Magnetic Resonance Imaging. Pediatr Cardiol 34, 1055–1056 (2013) doi:10.1007/s00246-012-0573-4

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Keywords

  • Isolated cleft mitral valve
  • Mitral regurgitation
  • Pulmonary atresia
  • Pulmonary varix
  • Ventricular septal defect