A ventriculoseptal defect (VSD) usually is present in patients with a double-outlet right ventricle. This report describes a case of double-outlet right ventricle with a completely shrouded inlet VSD and no interventricular shunting. This was associated with a severely regurgitant dysplastic mitral valve. The anatomy and clinical management of the patient is discussed together with an overview of the existing literature.
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Singla, M., Al-Radi, O. & Mertens, L. Double-Outlet Right Ventricle Without Interventricular Communication: An Unusual and Challenging Problem. Pediatr Cardiol 34, 1941–1944 (2013) doi:10.1007/s00246-012-0483-5
- Congenital heart disease
- Double-outlet right ventricle
- Rare defects