The absence of a right superior vena cava (SVC) in situs solitus is very rare, and even then it is usually associated with left SVC. There have been few case reports in the literature of isolated bilateral absence of SVC. Bilateral absent SVC can have clinical implication, including pacemaker placements, central venous line placement, monitoring, and occasionally associated anomalies. We describe a case detected on fetal echocardiogram with bilateral absent SVC and structurally normal heart.
This is a preview of subscription content, log in to check access.
Buy single article
Instant unlimited access to the full article PDF.
Price includes VAT for USA
Subscribe to journal
Immediate online access to all issues from 2019. Subscription will auto renew annually.
This is the net price. Taxes to be calculated in checkout.
Barrea C, Ovaert C, Moniotte S, Biard JM, Steenhaut P, Bernard P (2011) Prenatal diagnosis of abnormal cardinal systemic venous return without other heart defects: a case series. Prenat Diagn 31:380–388
Bartram U, Van Praagh S, Levine JC, Hines M, Bensky AS, Van Praagh R (1997) Absent right superior vena cava in visceroatrial situs solitus. Am J Cardiol 80:175–183
Choi JY, Anderson RH, Macartney FJ (1987) Absent right superior caval vein (vena cava) with normal atrial arrangement. Br Heart J 57:474–478
Hussain SA, Chakravarty S, Chaikhouni A, Smith JR (1981) Congenital absence of superior vena cava: unusual anomaly of superior systemic veins complicating pacemaker placement. Pacing Clin Electrophysiol 4:328–334
Krasemann T, Kehl G, Vogt J, Asfour B (2003) Unusual systemic venous return with complete absence of the superior caval veins. Pediatr Cardiol 24:397–399
Lee CY, Jan SL, Wang TM, Chi CS (2005) Congenital chylothorax associated with isolated congenital hypoplastic superior caval vein: a case report. Acta Paediatr 94:1840–1843
Marin-Garcia J, Sanmarti J, Moller JH (1978) Congenital absence of the right superior vena cava: report of two cases. Eur J Cardiol 7:293–297
Romer S, Opgen-Rhein B, Chaoui R, Scheer I, Czernik C, Obladen M (2006) Bilateral agenesis of the superior vena cava associated with congenital hydrothorax. Ultrasound Obstet Gynecol 28:842–844
Tacy TA, Silverman NH (2001) Systemic venous abnormalities: embryologic and echocardiographic considerations. Echocardiography 18:401–413
Electronic supplementary material
Below is the link to the electronic supplementary material.
About this article
Cite this article
Bansal, M., Strainic, J. & Ashwath, R. Bilateral Absence of Superior Vena Cava. Pediatr Cardiol 34, 1031–1033 (2013) doi:10.1007/s00246-012-0357-x
- Superior vena cava
- Congenital heart disease
- Fetal echocardiography