Cor triatriatum sinister is an uncommon congenital cardiac defect that has rarely been described in association with left-sided partial anomalous pulmonary venous return. We present a case of such rare anatomy with multilevel obstruction that presented in infancy as cardiogenic shock. The patient underwent staged treatment with extracorporeal membrane oxygenation stabilization, catheter-based balloon dilatation of the cor triatriatum and atrial septostomy, followed by definitive surgical repair, with excellent result.
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Schiller, O., Burns, K.M., Sinha, P. et al. Cor Triatriatum With Partial Anomalous Pulmonary Venous Return: A Rare Case of Parallel Obstruction and Successful Staged Treatment. Pediatr Cardiol 33, 363–365 (2012) doi:10.1007/s00246-011-0148-9
- Cor triatriatum
- Partial anomalous pulmonary venous return
- Pulmonary venous obstruction
- Cardiac catheterization
- Cardiac surgery