Pediatric Cardiology

, Volume 31, Issue 1, pp 1–6 | Cite as

Dextrocardia: Practical Clinical Points and Comments on Terminology

  • William N. Evans
  • Ruben J. Acherman
  • Juan C. Collazos
  • William J. Castillo
  • Robert C. Rollins
  • Katrinka T. Kip
  • Humberto Restrepo
Original Article


Dextrocardia is defined by the authors as a right-sided heart with a base–apex axis directed rightward, resulting from a variation in cardiac development, and not used as a general term indicating any heart in the right chest. Dextrocardia occurs in approximately 0.01% of live births and can be discovered in various clinical settings and at various patient ages. The authors review their experience with dextrocardia, discuss useful clinical points that aid in evaluating complex anatomy, recount the history of dextrocardia terminology, and note the current inconsistent nomenclature.


Dexiocardia Dextrocardia Heterotaxy Situs inversus Situs solitus 

Cardiac Segmental Abbreviations


Situs ambiguous, atrioventricular concordance, ventriculoarterial concordance, and normally related great arteries


Situs ambiguous, atrioventricular concordance, ventriculoarterial concordance, and normally related great arteries


Situs inversus, atrioventricular discordance, ventriculoarterial discordance, and D-transposition of the great arteries


Situs inversus, atrioventricular concordance, ventriculoarterial concordance, and normally related great arteries


Situs inversus, atrioventricular concordance, ventriculoaterial discordance, and L-transposition of the great arteries


Situs solitus, atrioventricular concordance, ventriculoarterial concordance, and normally related great arteries


Situs solitus, atrioventricular discordance, ventriculoarterial discordance, and L-transposition of the great arteries


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Copyright information

© Springer Science+Business Media, LLC 2009

Authors and Affiliations

  • William N. Evans
    • 1
    • 2
  • Ruben J. Acherman
    • 1
    • 2
  • Juan C. Collazos
    • 2
  • William J. Castillo
    • 1
    • 2
  • Robert C. Rollins
    • 1
    • 2
  • Katrinka T. Kip
    • 1
    • 2
  • Humberto Restrepo
    • 1
    • 2
  1. 1.Children’s Heart Center–NevadaLas VegasUSA
  2. 2.Division of Cardiology, Department of PediatricsUniversity of Nevada School of MedicineLas VegasUSA

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