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Herz

, Volume 44, Issue 6, pp 553–572 | Cite as

Medizinische Versorgung von Erwachsenen mit angeborenen Herzfehlern

Gegenwart und Zukunft
  • R. NeidenbachEmail author
  • S. Achenbach
  • C. Andonian
  • J. Beckmann
  • S. Biber
  • S. Dittrich
  • P. Ewert
  • S. Freilinger
  • M. Huntgeburth
  • N. Nagdyman
  • R. Oberhoffer
  • L. Pieper
  • Y. von Kodolitsch
  • M. Weyand
  • U. M. M. Bauer
  • H. KaemmererEmail author
CME
  • 326 Downloads

Zusammenfassung

Angeborene Herzfehler (AHF) sind die häufigsten angeborenen Organanomalien. Dank medizinischer Fortschritte erreichen heutzutage fast alle Patienten das Erwachsenenalter. Trotz primär erfolgreicher Behandlungen können Rest- und Folgezustände sowie (nicht-)kardiale Komorbiditäten den chronischen Krankheitsverlauf beeinflussen und zu einer erhöhten Morbidität und Mortalität führen. Erwachsene mit angeborenen Herzfehlern (EmaH) in Deutschland sind trotz des großen Nachsorgebedarfs nicht an die Versorgungsstrukturen angebunden. Daten der VEmaH-Studie („Versorgungssituation von EmaH“) belegen, dass EmaH und primär betreuende Haus- und Allgemeinärzte hinsichtlich des Komplikationspotenzials von AHF und der Notwendigkeit einer fachspezifischen Nachsorge enorme Informationsdefizite aufweisen. Eine optimierte, zukunftsorientierte Versorgung erfordert eine regelmäßige Nachsorge und die Möglichkeit zur fächerübergreifenden, integrierten medizinischen Versorgung von AHF im Langzeitverlauf.

Schlüsselwörter

Angeborene Herzfehlbildungen Kardiologie EmaH Komorbiditäten Prävention 

Medical care of adults with congenital heart diseases

Present and future

Abstract

Congenital heart diseases (CHD) are the most common types of congenital organ defects. Thanks to medical progress in congenital cardiology and heart surgery, most children with CHD reach adulthood. Despite primarily successful treatment residual and subsequent conditions as well as (non)cardiac comorbidities can influence the chronic course of the disease and lead to a higher morbidity and mortality. Adults with congenital heart disease (ACHD) in Germany are not tied to the healthcare structure despite the great need for aftercare. According to the results of the medical care of ACHD (MC-ACHD) study, ACHD centers and specialists in Germany are insufficiently perceived despite increased complication rates and the great need for specialist guidance. General practitioners and patients are not adequately informed about existing ACHD facilities. A better awareness of the ACHD problem should be created at the level of primary medical supply in order to optimize care and to reduce morbidity and mortality. Improved future-oriented patient care includes lifelong regular follow-up and the possibility of interdisciplinary, integrated medical care of CHD.

Keywords

Congenital heart defects Cardiology ACHD Comorbidities Prevention 

Notes

Danksagung

Wir danken der Deutschen Herzstiftung e. V. und Herzkind e. V. für die projektbezogene Förderung der Versorgungsforschung bei EmaH.

Einhaltung ethischer Richtlinien

Interessenkonflikt

R. Neidenbach, S. Achenbach, C. Andonian, J. Beckmann, S. Biber, S. Dittrich, P. Ewert, S. Freilinger, M. Huntgeburth, N. Nagdyman, R. Oberhoffer, L. Pieper, Y. von Kodolitsch, M. Weyand, U. M. M. Bauer und H. Kaemmerer erklären, dass sie sich bei der Erstellung des Beitrages von keinen wirtschaftlichen Interessen leiten ließen und dass keine potenziellen Interessenkonflikte vorliegen.

Für diesen Beitrag wurden von den Autoren keine Studien an Menschen oder Tieren durchgeführt. Für die aufgeführten Studien gelten die jeweils dort angegebenen ethischen Richtlinien.

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Copyright information

© Springer Medizin Verlag GmbH, ein Teil von Springer Nature 2019

Authors and Affiliations

  • R. Neidenbach
    • 1
    Email author
  • S. Achenbach
    • 2
  • C. Andonian
    • 3
  • J. Beckmann
    • 3
  • S. Biber
    • 3
  • S. Dittrich
    • 2
  • P. Ewert
    • 1
  • S. Freilinger
    • 1
  • M. Huntgeburth
    • 4
  • N. Nagdyman
    • 1
  • R. Oberhoffer
    • 5
  • L. Pieper
    • 6
  • Y. von Kodolitsch
    • 7
  • M. Weyand
    • 2
  • U. M. M. Bauer
    • 8
  • H. Kaemmerer
    • 1
    Email author
  1. 1.Klinik für angeborene Herzfehler und KinderkardiologieDeutsches Herzzentrum MünchenMünchenDeutschland
  2. 2.Medizinische Klinik 2, Kardiologie und AngiologieUniversitätsklinikum ErlangenErlangenDeutschland
  3. 3.Lehrstuhl für Sportpsychologie, Fakultät für Sport- und GesundheitswissenschaftenTechnische Universität MünchenMünchenDeutschland
  4. 4.Klinik III für Innere Medizin, Zentrum für Erwachsene mit angeborenen Herzfehlern (EMAH), HerzzentrumUniversitätsklinikum KölnKölnDeutschland
  5. 5.Lehrstuhl für Präventive PädiatrieTechnische Universität MünchenMünchenDeutschland
  6. 6.Professur für behaviorale EpidemiologieTechnische Universität DresdenDresdenDeutschland
  7. 7.Universitäres Herzzentrum Hamburg, Klinik und Poliklinik für Allgemeine und Interventionelle KardiologieUniversitätsklinikum Hamburg-EppendorfHamburgDeutschland
  8. 8.Nationales Register für angeborene HerzfehlerBerlinDeutschland

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