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Tumeurs carcinoïdes familiales à localisation rectale

Familial carcinoid rectal tumours

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Les tumeurs carcinoïdes digestives familiales sont très rares et la localisation rectale n’a été décrite qu’une fois dans la littérature. A ce propos, nous rapportons 2 cas de tumeurs carcinoïdes rectales survenant chez une fratrie de premier degré, caractérisés par une localisation au niveau du bas rectum et une taille < 2 cm. La résection chirurgicale est suivie d’une évolution favorable sans récidive locorégionale à 5 ans pour la sœur et à 3 ans pour le frère.


The familial digestive carcinoids are very uncommon and the rectal localization was reported once in the literature. We report a familial rectal carcinoids occurring in two siblings characterized by a localization in low rectum and a size < 2 cm. The surgical resection was followed by a favorable evolution without locoregional reccurence after 5 years for the sister and 3 years for the brother. Tirés à part : Nawal KABBAJ, 4 lotissement Anne-Marie, avenue Bir Kacem, rue Ouled Farés, Souissi, Rabat (Maroc).

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Correspondence to Nawal Kabbaj.

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Kabbaj, N., Guedira, M., El Atmani, H. et al. Tumeurs carcinoïdes familiales à localisation rectale. Acta Endosc 36, 755 (2006). https://doi.org/10.1007/BF03018518

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  • carcinoïde
  • cas familiaux
  • rectum
  • tumeur


  • carcinoid tumours
  • familial cases
  • rectum