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Melanotic paraganglioma of the orbit: a case report


A paraganglioma of the orbit in a 21-year-old woman is presented, containing oculo-cutaneous melanin in many tumor cells, occasionally adjacent to neurosecretory granules, and in macrophages. This tumor expands the list of neuroectodermal tumors with potential melaninization.

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Correspondence to K. Jellinger.

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Paulus, W., Jellinger, K. & Brenner, H. Melanotic paraganglioma of the orbit: a case report. Acta Neuropathol 79, 340–346 (1989).

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Key words

  • Paraganglioma
  • Melanin
  • Orbit
  • Immunocytochemistry
  • Electron microscopy