1. Hugo and Ann Moser: A Unique Husband and Wife Team

   • Joseph M. Tager

   Foreword Pages: 463 - 464

2. Hugo and Ann: A Perfect Partnership

   • Marjorie B. Lees

   OriginalPaper Pages: 465 - 469

3. Drastically Abnormal Gluco- and Galactosylceramide Composition Does Not Affect Ganglioside Metabolism in the Brain of Mice Deficient in Galactosylceramide Synthase

   • Kunihiko Suzuki
   • Marie T. Vanier
   • Brian Popko

   OriginalPaper Pages: 471 - 474

4. G_M2-Ganglioside Metabolism In Situ in Mucolipidosis IV Fibroblasts

   • S. Raghavan
   • E. Leshinsky
   • E.H. Kolodny

   OriginalPaper Pages: 475 - 479

5. Lipid Changes in Niemann-Pick Disease Type C Brain: Personal Experience and Review of the Literature

   • Marie T. Vanier

   OriginalPaper Pages: 481 - 489

6. Demyelinating Disease: Evolution of a Paradigm

   • Byron H. Waksman

   OriginalPaper Pages: 491 - 495

7. The G1 Restriction Point as Critical Regulator of Neocortical Neuronogenesis

   • V.S. Caviness Jr.
   • T. Takahashi
   • R.S. Nowakowski

   OriginalPaper Pages: 497 - 506

8. Biochemistry and Molecular Biology of Canavan Disease

   • Reuben Matalon
   • Kimberlee Michals-Matalon

   OriginalPaper Pages: 507 - 513

9. On the Front of X-Linked Adrenoleukodystrophy

   • Patrick Aubourg

   OriginalPaper Pages: 515 - 520

10. X-Linked Adrenoleukodystrophy: Genes, Mutations, and Phenotypes

    • Kirby D. Smith
    • Stephan Kemp
    • Paul A. Watkins

    OriginalPaper Pages: 521 - 535

11. Leukodystrophy and Bone Marrow Transplantation: Role of Mixed Hematopoietic Chimerism

    • Christina L. Kaufman
    • Suzanne T. Ildstad

    OriginalPaper Pages: 537 - 549

12. Peroxisomal β-Oxidation Enzymes

    • Takashi Hashimoto

    OriginalPaper Pages: 551 - 563

13. Peroxisomal Disorders: Clinical, Biochemical, and Molecular Aspects

    • Ronald J.A. Wanders

    OriginalPaper Pages: 565 - 580

14. Rhizomelic Chondrodysplasia Punctata, a Peroxisomal Biogenesis Disorder Caused by Defects in Pex7p, a Peroxisomal Protein Import Receptor: A Minireview

    • P. Edward Purdue
    • Marek Skoneczny
    • Paul B. Lazarow

    OriginalPaper Pages: 581 - 586

15. Defective Glucose Transport Across Brain Tissue Barriers: A Newly Recognized Neurological Syndrome

    • Jörg Klepper
    • Dong Wang
    • Darryl C. De Vivo

    OriginalPaper Pages: 587 - 594

16. Molecular Mechanisms of Lead Neurotoxicity

    • Joseph Bressler
    • Kyung-ah Kim
    • Gary Goldstein

    OriginalPaper Pages: 595 - 600

17. Gene Transfer Approaches to the Lysosomal Storage Disorders

    • John A. Barranger
    • Erin O. Rice
    • William P. Swaney

    OriginalPaper Pages: 601 - 615