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Idiopathic Interstitial Pneumonia and Connective Tissue Disease-Associated Interstitial Lung Disease: Similarities and Differences

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Idiopathic Pulmonary Fibrosis

Part of the book series: Respiratory Medicine ((RM,volume 9))

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Abstract

Determining whether an “idiopathic” interstitial pneumonia (IP) is actually a manifestation of an underlying connective tissue disease (CTD) is important, because this knowledge often has a significant impact on management and prognosis. The detection of occult CTD (and distinguishing these cases from idiopathic disease) is challenging and can be optimized by a thorough and multidisciplinary evaluation. In this chapter, we discuss the complex intersection that exists between CTD and interstitial lung disease (ILD) and highlight specific clinical, laboratory, radiologic, and histopathologic features that are useful in distinguishing CTD-associated ILD from idiopathic interstitial pneumonia (IIP).

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Author information

Authors and Affiliations

  1. Department of Medicine, Autoimmune and Interstitial Lung Disease Program, National Jewish Health, Denver, CO, USA

    Joshua J. Solomon M.D.

  2. Division of Rheumatology, Department of Medicine, Autoimmune and Interstitial Lung Disease Program, National Jewish Health, 1400 Jackson Street, Denver, CO, 80206, USA

    Aryeh Fischer M.D.

Authors
  1. Joshua J. Solomon M.D.
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  2. Aryeh Fischer M.D.
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Corresponding author

Correspondence to Aryeh Fischer M.D. .

Editor information

Editors and Affiliations

  1. Dept. Internal Medicine, Sect. Allergy Pulmonary & Critical Care Med., University of Wisconsin School of Medicine & Public Health, Madison, Wisconsin, USA

    Keith C. Meyer

  2. Advanced Lung Disease and Lung Transplant Program, Inova Fairfax Hospital, Falls Church, Virginia, USA

    Steven D. Nathan

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Solomon, J.J., Fischer, A. (2014). Idiopathic Interstitial Pneumonia and Connective Tissue Disease-Associated Interstitial Lung Disease: Similarities and Differences. In: Meyer, K., Nathan, S. (eds) Idiopathic Pulmonary Fibrosis. Respiratory Medicine, vol 9. Humana Press, Totowa, NJ. https://doi.org/10.1007/978-1-62703-682-5_11

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  • DOI: https://doi.org/10.1007/978-1-62703-682-5_11

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  • Publisher Name: Humana Press, Totowa, NJ

  • Print ISBN: 978-1-62703-681-8

  • Online ISBN: 978-1-62703-682-5

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